McCune-Albright syndrome: a case report and review

Ayesha Asmal, William Greig Evans

Abstract


McCune-Albright syndrome is a rare condition. Patients may present with polyostotic fibrous dysplasia, have café-au lait spots on the skin and evident endocrinopathies, the most common being precocious puberty which is probably an early diagnostic sign. This case report is of a 15 year-old male who presented for dental treatment and was diagnosed with the syndrome. Radiological examination revealed characteristic bony dysplasia in his mandible and maxilla. Periodic radiographic evaluations, including cone-beam computed tomography (CBCT), were performed over the next three years. The images showed the expected slight recession of his bony lesions. 

 

Lay abstract

This is a case report of a male teenager who presented with dental problems and was found to have irregular tissue in his jaw and also creamy-brown spots on his skin. His pathology presented challenges to management and treatment options.


Keywords


fibrous dysplasia, polyostotic lesions, cone beam computed tomography

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The South African Radiographer | ISSN 0258 0241

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