McCune-Albright syndrome: a case report and review

Authors

Keywords:

fibrous dysplasia, polyostotic lesions, cone beam computed tomography

Abstract

McCune-Albright syndrome is a rare condition. Patients may present with polyostotic fibrous dysplasia, have café-au lait spots on the skin and evident endocrinopathies, the most common being precocious puberty which is probably an early diagnostic sign. This case report is of a 15 year-old male who presented for dental treatment and was diagnosed with the syndrome. Radiological examination revealed characteristic bony dysplasia in his mandible and maxilla. Periodic radiographic evaluations, including cone-beam computed tomography (CBCT), were performed over the next three years. The images showed the expected slight recession of his bony lesions. 

 

Lay abstract

This is a case report of a male teenager who presented with dental problems and was found to have irregular tissue in his jaw and also creamy-brown spots on his skin. His pathology presented challenges to management and treatment options.

Author Biographies

Ayesha Asmal, School of Oral Health Sciences University of Witwatersrand Johannesburg

Radiology Unit, Department of General Dental Practice

Radiographer

William Greig Evans, School of Oral Health Sciences University of Witwatersrand Johannesburg

Department of Orthodontics

Visiting Professor

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Published

2020-11-16

Issue

Vol. 58 No. 2 (2020)

Section

Case Reports

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